Auditory Steady-State Responses in Children with Auditory Neuropathy: A Four-Case Series

A case series presents auditory steady-state response (ASSR) findings from four children diagnosed with auditory neuropathy (AN), aged 3 weeks to 33 months. The data, authored by Leigh Biagio de Jager and last updated in May 2026, is a 31.5 KB DOCX document hosted on figshare. It discusses discordant findings between ASSR and auditory brainstem response (ABR) tests and postulates the summating potential as a source of the measured responses.

Use Cases

• Analyzing patterns of discordance between ASSR and ABR findings based on the described case series.
• Investigating the origin of ASSR signals in cases of auditory neuropathy based on the postulated summating potential source.
• Evaluating the reliability of ASSR for predicting behavioral hearing thresholds in AN patients based on the described limitations.
• Studying pre-neural cochlear activity in pediatric auditory neuropathy cases based on the described electrophysiological responses.

Strengths

• Focuses on a specific and rare clinical condition (auditory neuropathy) with four detailed pediatric cases.
• Provides theoretical discussion and systematic elimination of potential response origins based on empirical evidence.
• Dataset is openly available under a CC-BY-NC-ND-4.0 license.

Limitations

• Dataset scale is very limited, containing only four cases in a 31.5 KB document.
• Column-level documentation is absent; field semantics must be inferred from the narrative description.
• Row count is unknown, which may limit suitability assessment for quantitative analysis.

Provenance

Source

figshare

Collection Method

Clinical case series.

Freshness

Last updated 2026-05-14 17:56:26